Dr. Ronald Chin’s Explanation Of Congenital Sensorineural Hearing Loss

Dr. Ronald Chin’s Explanation Of Congenital Sensorineural Hearing Loss

Congenital sensorineural hearing loss is an inner ear hearing loss that is present at birth. It can be either hereditary or non-hereditary. The hereditary defects can be classified as non-syndrome-associated and syndrome-associated.

65% of the cases are non-syndrome-associated. These include hearing impairment and autosomal recessive traits. And 35% of the cases are syndrome-associated. These include Charge syndrome, Alport syndrome, Waardenburg syndrome, and Teacher Collins syndrome.

Non-hereditary defects cause direct damage to the developing cochlea, which include intrauterine infections, teratogens, and medications. Factors related to the inner ear are prematurity, kernicterus, family history of childhood hearing impairment, and hypoxia.

Glue ear, after draining the ear drum

Glue ear, intact ear drum

X